PDF(Pubmed)
Abstract：
UNASSIGNED: Solid pseudopapillary tumor is a low-grade malignancy of the pancreas and predominantly affects young women. This neoplasm is a rare pancreatic entity with vague clinical presentation. Diagnosis is often incidental through imaging or even during surgical approach for another condition.
UNASSIGNED: A 22-year-old Brazilian female with gastrointestinal symptoms was diagnosed with achalasia and underwent Heller myotomy. Intraoperatory findings included an enlarging mass in the distal pancreas. During follow-up for the surgical approach of achalasia, a hypothesis of Frantz\'s tumor was stated, and spleen-preserving distal pancreatectomy was performed.
UNASSIGNED: The pathological pathways of Frantz\'s tumor is still unclear, and its connection with chromosomal abnormalities is under investigation. Although the tumor has been reclassified over the years to solid pseudopapillary tumor, surgical resection remains the standard treatment.
UNASSIGNED: Despite a surgical challenge, surgery presents a great prognosis in these patients and long-term survival. High suspicion and proper investigation are fundamental to diagnosis and early treatment.
UNASSIGNED: A 22-year-old Brazilian female with gastrointestinal symptoms was diagnosed with achalasia and underwent Heller myotomy. Intraoperatory findings included an enlarging mass in the distal pancreas. During follow-up for the surgical approach of achalasia, a hypothesis of Frantz\'s tumor was stated, and spleen-preserving distal pancreatectomy was performed.
UNASSIGNED: The pathological pathways of Frantz\'s tumor is still unclear, and its connection with chromosomal abnormalities is under investigation. Although the tumor has been reclassified over the years to solid pseudopapillary tumor, surgical resection remains the standard treatment.
UNASSIGNED: Despite a surgical challenge, surgery presents a great prognosis in these patients and long-term survival. High suspicion and proper investigation are fundamental to diagnosis and early treatment.
摘要：
■实性假乳头状瘤是胰腺的低度恶性肿瘤，主要影响年轻女性。这种肿瘤是一种罕见的胰腺实体，临床表现模糊。诊断通常是偶然的通过成像或甚至在手术方法的另一种情况。
一名22岁的巴西女性出现胃肠道症状，被诊断为贲门失弛缓症，并接受了Heller肌切开术。术中发现包括远端胰腺肿块增大。在贲门失弛缓症手术入路的随访中，Frantz’s肿瘤的假设被陈述，并进行了保留脾脏的远端胰腺切除术。
■Frantz肿瘤的病理通路尚不清楚，它与染色体异常的联系正在调查中。尽管多年来肿瘤已被重新分类为实性假乳头状瘤，手术切除仍然是标准治疗。
■尽管面临手术挑战，手术在这些患者中具有良好的预后和长期生存。高度怀疑和适当的调查是诊断和早期治疗的基础。
一名22岁的巴西女性出现胃肠道症状，被诊断为贲门失弛缓症，并接受了Heller肌切开术。术中发现包括远端胰腺肿块增大。在贲门失弛缓症手术入路的随访中，Frantz’s肿瘤的假设被陈述，并进行了保留脾脏的远端胰腺切除术。
■Frantz肿瘤的病理通路尚不清楚，它与染色体异常的联系正在调查中。尽管多年来肿瘤已被重新分类为实性假乳头状瘤，手术切除仍然是标准治疗。
■尽管面临手术挑战，手术在这些患者中具有良好的预后和长期生存。高度怀疑和适当的调查是诊断和早期治疗的基础。
