PDF(Pubmed)
Abstract：
BACKGROUND: Macrodactyly is a rare congenital malformation characterized by an increase in the size of all structures of a digit, accounting for less than 1% of all congenital upper extremity conditions.
METHODS: We report a case involving a 49-year-old woman who presented for the first time with untreated, radial-sided hand macrodactyly. We performed soft tissue debulking, amputation, median nerve neurotomy and coaptation, and carpal tunnel release. At the 6-year follow-up, no significant growth was observed in the bone or soft tissue of the affected area.
CONCLUSIONS: Tissue overgrowth in patients with progressive macrodactyly can continue and progress excessively with age. Median nerve neurotomy and coaptation play a crucial role in preventing recurrence of the deformity.
METHODS: We report a case involving a 49-year-old woman who presented for the first time with untreated, radial-sided hand macrodactyly. We performed soft tissue debulking, amputation, median nerve neurotomy and coaptation, and carpal tunnel release. At the 6-year follow-up, no significant growth was observed in the bone or soft tissue of the affected area.
CONCLUSIONS: Tissue overgrowth in patients with progressive macrodactyly can continue and progress excessively with age. Median nerve neurotomy and coaptation play a crucial role in preventing recurrence of the deformity.
摘要：
背景：Macrodactyly是一种罕见的先天性畸形，其特征是手指所有结构的大小都增加，占所有先天性上肢疾病的不到1％。
方法：我们报告一例49岁女性首次出现未治疗，径向侧手宏观。我们做了软组织减积术,截肢,正中神经切断术和接合，腕管松解术.在6年的随访中，在受影响区域的骨骼或软组织中未观察到明显的生长。
结论：进行性大指患者的组织过度生长可以随着年龄的增长而持续和过度发展。正中神经切开术和接合在预防畸形复发中起着至关重要的作用。
方法：我们报告一例49岁女性首次出现未治疗，径向侧手宏观。我们做了软组织减积术,截肢,正中神经切断术和接合，腕管松解术.在6年的随访中，在受影响区域的骨骼或软组织中未观察到明显的生长。
结论：进行性大指患者的组织过度生长可以随着年龄的增长而持续和过度发展。正中神经切开术和接合在预防畸形复发中起着至关重要的作用。
