PDF(Pubmed)
Abstract：
UNASSIGNED: Epithelioid angiomyolipoma (EAML), a subtype of angiomyolipoma, is distinct. It has a biologic behavior of borderline tumor, a malignant tendency, and a risk of metastasis and recurrence. Adrenal EAML is very rare. It is true that only six cases of adrenal EAML have been documented in the English-language literature.
UNASSIGNED: A 65-year-old man who underwent a laparoscopic left adrenalectomy in July 2022 has adrenal EAML and this is a case report about it. The mass was surrounded by abundant blood vessels and adherence with surround-tissue. Postoperative pathology of the tumor analysis revealed adrenal epithelioid vascular smooth muscle lipoma. The patient underwent left upper abdomen and lumbar pain in July 2022. The enhanced computed tomography (CT) scan of the abdomen showed markedly enhanced masses in and around the left adrenal gland. A second left laparoscopic adrenalectomy was performed under general anesthesia. Postoperative pathology showed two taupe nodules of left adrenal, maximum diameter 0.9 to 1.1 cm. The postoperative pathological diagnosis in combination with immunohistochemistry was EAML. The patient was discharged 10 days later with symptomatic treatment with low molecular heparin.
UNASSIGNED: Adrenal EAML has a biologic behavior of borderline tumor with malignant potential and a risk of distant metastasis and recurrence. Therefore, radical surgical resection should be considered as its necessary treatment. Long-term postoperative follow-up is an important part of the treatment.
UNASSIGNED: A 65-year-old man who underwent a laparoscopic left adrenalectomy in July 2022 has adrenal EAML and this is a case report about it. The mass was surrounded by abundant blood vessels and adherence with surround-tissue. Postoperative pathology of the tumor analysis revealed adrenal epithelioid vascular smooth muscle lipoma. The patient underwent left upper abdomen and lumbar pain in July 2022. The enhanced computed tomography (CT) scan of the abdomen showed markedly enhanced masses in and around the left adrenal gland. A second left laparoscopic adrenalectomy was performed under general anesthesia. Postoperative pathology showed two taupe nodules of left adrenal, maximum diameter 0.9 to 1.1 cm. The postoperative pathological diagnosis in combination with immunohistochemistry was EAML. The patient was discharged 10 days later with symptomatic treatment with low molecular heparin.
UNASSIGNED: Adrenal EAML has a biologic behavior of borderline tumor with malignant potential and a risk of distant metastasis and recurrence. Therefore, radical surgical resection should be considered as its necessary treatment. Long-term postoperative follow-up is an important part of the treatment.
摘要：
■上皮样血管平滑肌脂肪瘤（EAML），血管平滑肌脂肪瘤的一种亚型,是截然不同的。它具有交界性肿瘤的生物学行为，恶性倾向，和转移和复发的风险。肾上腺EAML非常罕见。的确，英语文献中只记录了6例肾上腺EAML。
一名65岁的男子在2022年7月接受了腹腔镜左肾上腺切除术，患有肾上腺EAML，这是一例病例报告。肿块被丰富的血管包围，并与周围组织粘连。术后肿瘤病理分析提示肾上腺上皮样血管平滑肌脂肪瘤。2022年7月，患者出现左上腹部和腰椎疼痛。腹部增强的计算机断层扫描（CT）扫描显示左肾上腺及其周围的肿块明显增强。在全身麻醉下进行了第二次左腹腔镜肾上腺切除术。术后病理示：左肾上腺灰褐色结节2个。最大直径0.9至1.1厘米。术后病理联合免疫组化诊断为EAML。10天后患者出院，给予低分子肝素对症治疗。
■肾上腺EAML具有具有恶性潜能的交界性肿瘤的生物学行为，并有远处转移和复发的风险。因此,根治性手术切除应被视为其必要的治疗方法。术后远期随访是治疗的重要环节。
一名65岁的男子在2022年7月接受了腹腔镜左肾上腺切除术，患有肾上腺EAML，这是一例病例报告。肿块被丰富的血管包围，并与周围组织粘连。术后肿瘤病理分析提示肾上腺上皮样血管平滑肌脂肪瘤。2022年7月，患者出现左上腹部和腰椎疼痛。腹部增强的计算机断层扫描（CT）扫描显示左肾上腺及其周围的肿块明显增强。在全身麻醉下进行了第二次左腹腔镜肾上腺切除术。术后病理示：左肾上腺灰褐色结节2个。最大直径0.9至1.1厘米。术后病理联合免疫组化诊断为EAML。10天后患者出院，给予低分子肝素对症治疗。
■肾上腺EAML具有具有恶性潜能的交界性肿瘤的生物学行为，并有远处转移和复发的风险。因此,根治性手术切除应被视为其必要的治疗方法。术后远期随访是治疗的重要环节。
