关键词: Acute abdomen Paediatric surgery Rhabdomyosarcoma

来  源:   DOI:10.1308/rcsann.2024.0065

Abstract:
Rhabdomyosarcoma (RMS) is a form of soft tissue sarcoma that can arise from muscle or fibrous tissue almost anywhere in the body. The two major subtypes of RMS are alveolar and embryonal, whereas the two rarer subtypes are pleomorphic, which typically occurs in adults, and the spindle cell/sclerosing variant, typically seen in children. RMS usually involves the extremities, the head and neck or the genitourinary system. Although it can arise from anywhere in the body, other sites of involvement are rare and usually present only at an advanced stage owing to a mass effect on surrounding tissues and organs. We present a rare case of a child who presented with the signs and symptoms of an acute abdomen, but intraoperatively was found to have a bleeding necrotic mass arising from the anterior abdominal wall. This was histologically confirmed to be a RMS of the embryonal type.
摘要:
横纹肌肉瘤(RMS)是软组织肉瘤的一种形式,几乎可以从身体任何地方的肌肉或纤维组织中产生。RMS的两个主要亚型是肺泡和胚胎,而这两个罕见的亚型是多形性的,这通常发生在成年人身上,和梭形细胞/硬化变体,通常见于儿童。RMS通常涉及四肢,头颈部或泌尿生殖系统。虽然它可以从身体的任何地方产生,其他受累部位很少见,由于对周围组织和器官的质量影响,通常仅在晚期出现。我们介绍了一个罕见的病例,儿童出现了急腹症的体征和症状,但术中发现前腹壁有出血坏死肿块。这在组织学上被证实是胚胎型的RMS。
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