Abstract:
Transverse vaginal septum (TVS) is a rare obstructive genital tract anomaly. It is associated with primary amenorrhoea and typically presents with cyclical abdominal pain due to obstruction of the menstrual flow. Caudal regression syndrome (CRS) is also a rare congenital anomaly that is frequently associated with anomalies of the neurological, musculoskeletal, cardiac, genitourinary and gastrointestinal systems. Obstructive genital tract anomaly in CRS is exceptionally rare. This report describes the case of a girl in early adolescence with underlying CRS who presented with severe abdominal pain associated with primary amenorrhoea. Clinical and radiological assessment revealed \'haematocolpos\' manifesting as a tender 20 weeks\' size abdominal mass and an absent vaginal opening. TVS was identified during examination under anaesthesia. The patient subsequently underwent a successful vaginoplasty with no recurrence of symptoms after 2 years.
摘要:
横向阴道隔(TVS)是一种罕见的阻塞性生殖道异常。它与原发性闭经有关,通常由于月经流阻塞而出现周期性腹痛。尾回归综合征(CRS)也是一种罕见的先天性异常,通常与神经系统异常有关。肌肉骨骼,心脏,泌尿生殖系统和胃肠道系统。CRS中的梗阻性生殖道异常极为罕见。本报告描述了一名青春期早期患有CRS的女孩的病例,该女孩表现出与原发性闭经相关的严重腹痛。临床和放射学评估显示,“血球”表现为20周大小的腹部肿块和无阴道开放。在麻醉下的检查期间鉴定出TVS。患者随后进行了一次成功的阴道成形术,2年后症状没有复发。