PDF(Pubmed)
Abstract：
Intraventricular schwannomas are extremely rare, typically benign tumors originating from Schwann cells, which are not normally found within the ventricular system. Their presence challenges conventional understanding of tumor origins and complicates diagnosis and management. We report the case of a 19-year-old female presenting with a drop attack and headache, with no significant medical history. MRI revealed a heterogeneously enhancing lesion in the right lateral ventricle. Differential diagnoses included malignant tumors; however, histopathological examination post-surgical resection confirmed an intraventricular schwannoma. Postoperative outcomes were favorable, with successful CSF diversion via a right occipital ventriculoperitoneal shunt for isolated right temporal hydrocephalus. This case is notable for its atypical presentation in a young patient, challenging the conventional understanding that intraventricular schwannomas primarily affect older individuals. In addition, the correct diagnosis and successful management of a rare intraventricular schwannoma underscores the importance of considering this rare diagnosis in patients with nonspecific neurological symptoms and intraventricular lesions. This case, alongside the literature review, enriches the body of evidence on intraventricular schwannomas, highlighting the critical role of surgical intervention and the need for a comprehensive diagnostic approach.
摘要：
脑室神经鞘瘤极为罕见，通常来源于雪旺氏细胞的良性肿瘤，通常不会在心室系统中发现。它们的存在挑战了对肿瘤起源的传统理解，并使诊断和管理复杂化。我们报道了一名19岁女性出现跌落发作和头痛的病例，没有明显的病史。MRI显示右侧脑室有不均匀增强的病变。鉴别诊断包括恶性肿瘤；然而，手术切除后的组织病理学检查证实为脑室内神经鞘瘤。术后结果良好，通过右枕脑室腹腔分流术成功分流脑脊液，治疗孤立的右颞叶脑积水。该病例以年轻患者的非典型表现而著称，挑战传统的理解，脑室内神经鞘瘤主要影响老年人。此外,对罕见的脑室内神经鞘瘤的正确诊断和成功治疗强调了在有非特异性神经症状和脑室内病变的患者中考虑这种罕见诊断的重要性.这个案子,在文献综述的同时，丰富了脑室内神经鞘瘤的证据，强调手术干预的关键作用和全面诊断方法的必要性。
