PDF(Pubmed)
Abstract：
Chiari malformations (CM) are a spectrum of hindbrain abnormalities involving the cerebellum, brainstem, skull base, and cervical cord. The most common is Chiari I malformation, in which the cerebellar tonsils descend through the foramen magnum. As opposed to types II-IV, which are congenital, type I can manifest in late childhood or adulthood with headaches and focal neurological symptoms. It can be caused by genetic variation, conditions that alter the basal skull or increase intracranial pressure, and even injury. Syringohydromyelia (SHM) is a neurological disorder characterized by longitudinal dilation of the central canal of the spinal cord with accumulated cerebrospinal fluid. This case report demonstrates a 35-year-old male with headaches, neck pain, back pain, and paresthesias who was found to have CM type-I malformation and syringohydromyelia.
摘要：
Chiari畸形（CM）是一系列涉及小脑的后脑异常，脑干,颅底,和颈索。最常见的是ChiariI畸形,小脑扁桃体通过大孔下降。与II-IV型相反，这是先天性的，I型可在儿童晚期或成年期出现头痛和局灶性神经症状。它可能是由遗传变异引起的，改变基底颅骨或增加颅内压的条件，甚至受伤。脊髓积水症（SHM）是一种神经系统疾病，其特征是脊髓中央管的纵向扩张，脑脊液积聚。此病例报告显示，一名35岁的男性患有头痛，颈部疼痛,背痛,和感觉异常，被发现患有CMI型畸形和紫癜性脊髓。
