PDF(Pubmed)
Abstract：
Chylothorax is a severe complication following the Fontan procedure, causing significant morbidity and mortality due to nutritional depletion and fluid loss. We present a case involving a six-year-old girl with tricuspid atresia, atrial septal defect (ASD), ventricular septal defect (VSD), and severe pulmonary stenosis (PS), presenting with fever, non-productive cough, and increased work of breathing. Cyanosis was noted, improving with oxygen. Imaging revealed bilateral pleural effusion, with pleural fluid analysis confirming chylothorax. Despite normal laboratory reports, retrograde transvenous lymphangiography indicated thoracic duct leakage. The patient underwent successful thoracic duct embolization, resulting in the resolution of the effusion and stabilization of her condition. She was discharged in a stable state, with follow-up care.
摘要：
乳糜胸是Fontan手术后的严重并发症，导致显著的发病率和死亡率由于营养消耗和液体流失。我们提出了一个六岁女孩三尖瓣闭锁的案例，房间隔缺损(ASD),室间隔缺损(VSD),和严重的肺动脉狭窄（PS），出现发烧，非生产性咳嗽,增加呼吸工作。注意到发霉，用氧气改善影像学显示双侧胸腔积液，胸膜液分析证实乳糜胸。尽管实验室报告正常,逆行经静脉淋巴管造影提示胸导管渗漏。患者行成功的胸导管栓塞术,导致积液的解决和病情的稳定。她在稳定状态下出院了,后续护理。
