PDF(Pubmed)
Abstract：
Renal angiomyolipoma (AML) is a rare benign tumor that follows an autosomal dominant inheritance pattern. Its association with polycystic kidney disease is uncommon, with only a handful of cases documented in the literature. The growth of lesions to a significant size may lead to life-threatening complications. We report a case of a 32-year-old female who presented with a palpable mass and bilateral flank pain. Following clinical assessment and CT examination, the patient underwent a left radical nephrectomy. The resected mass measured 9.3 x 8.2 x 7.5 cm, and the subsequent histopathological examination confirmed the diagnosis as renal AML.
摘要：
肾血管平滑肌脂肪瘤（AML）是一种罕见的良性肿瘤，遵循常染色体显性遗传模式。它与多囊肾病的关系并不常见，文献中只有少数案例记录。病变增长到显著的尺寸可能导致危及生命的并发症。我们报告了一例32岁女性，表现出明显的肿块和双侧腹部疼痛。在临床评估和CT检查后，患者接受了左侧根治性肾切除术.切除的质量测量为9.3x8.2x7.5厘米，随后的组织病理学检查证实诊断为肾AML。
