Abstract：
The primary purpose of this study was to enhance the understanding of diastematomyelia, with a particular focus on adult-onset cases, which are infrequent and not fully elucidated. Additionally, the study sought to analyse the clinical features, diagnostic characteristics, and surgical interventions employed to manage the condition. This retrospective case series aimed to investigate diastematomyelia, a rare congenital deformation affecting the spinal cord. The study included 16 patients diagnosed with diastematomyelia, consisting of 13 pediatric cases (mean age: 7.6 years, age range: 5 months to 13 years) and 3 adult cases (mean age: 36 years, age range: 26 to 48 years). Among the paediatric cases, 9 were females, and 4 were males, while the adult cohort comprised 2 males and 1 female. The study design involved a thorough review of medical records, imaging reports, and surgical outcomes without specific inclusion or exclusion criteria. Surgical intervention emerged as the primary treatment modality for all cases, except one. Following surgical intervention, significant improvements were observed in pain management, motor function, and bladder control. Furthermore, additional findings indicated the presence of Dural Ectasia and Vertebral segmentation defects among the study population. This retrospective case series sheds light on the clinical features and surgical outcomes of diastematomyelia in both pediatric and adult patients. The findings underscore the importance of surgical intervention in alleviating symptoms and enhancing motor coordination and bladder control.
摘要：
这项研究的主要目的是加强对脊髓纵裂的理解，特别关注成人发病病例，这是罕见的，没有完全阐明。此外,这项研究试图分析临床特征，诊断特征，以及用于控制病情的手术干预措施。这个回顾性病例系列旨在调查脊髓纵裂，一种罕见的影响脊髓的先天性变形。该研究包括16例诊断为脊髓纵裂的患者，由13例儿科病例组成（平均年龄：7.6岁，年龄范围：5个月至13岁）和3例成人病例（平均年龄：36岁，年龄范围：26至48岁）。在儿科病例中，9是女性，四个是男性，而成人队列包括2名男性和1名女性。研究设计包括全面审查医疗记录，成像报告,和无特定纳入或排除标准的手术结局。手术干预成为所有病例的主要治疗方式，除了一个。手术干预后，在疼痛管理方面观察到显着改善，运动功能,和膀胱控制。此外，其他研究结果表明,研究人群中存在硬膜扩张和椎体分割缺损.此回顾性病例系列揭示了小儿和成人患者脊髓纵裂的临床特征和手术结果。研究结果强调了手术干预在减轻症状，增强运动协调和膀胱控制方面的重要性。
