PDF(Pubmed)
Abstract：
Conductive hearing loss with a normal tympanic membrane is a common reason for otolaryngology consultation, with otospongiosis being the most frequent cause and House syndrome being extremely rare, requiring systematic investigation. We report the case of a 31-year-old woman who presented with conductive hearing loss with a normal tympanic membrane. A temporal bone computed tomography (CT) scan confirmed a House-Goodhill syndrome due to fixation of the malleus head. Surgical intervention was considered to remove the attic bone synostosis with the malleus head, resulting in a significant clinical improvement. The Goodhill syndrome is a rare condition that causes hearing loss with a normal eardrum. The surgery can highly improve the hearing function.
摘要：
鼓膜正常的传导性听力损失是耳鼻喉科咨询的常见原因，耳海绵症是最常见的原因，豪斯综合症极为罕见，需要系统的调查。我们报告了一例31岁的女性，其表现为鼓膜正常的传导性听力损失。颞骨计算机断层扫描（CT）扫描证实了由于锤头固定而导致的House-Goodhill综合征。手术干预被认为是用锤头去除阁楼骨融合，导致临床明显改善。Goodhill综合征是一种罕见的疾病，可导致正常耳膜的听力损失。手术可以极大地改善听力功能。
