PDF(Pubmed)
Abstract：
Mucinous cystic neoplasm of the liver (MCN-L) is a rare tumor which accounts for less than 5% of all liver cysts. Although they are considered to be \"benign cysts\" radiologically and clinically because of their slow growth, they are considered as premalignant. We present two radiologically misdiagnosed cases that operated in a short time range, in order to increase awareness for these rare tumors. A 47-year-old female patient who had no active complaints 58 x 40 mm cystic lesion was detected in the liver, which was diagnosed hydatid cyst radiologically. The pathological examination showed multiloculated cysts which was covered by low-grade mucinous epithelium and ovarian-type stroma on the cyst wall. A 50-year-old female patient presented with abdominal distention. The radiographical screening revealed a 204 x 140 mm cystic lesion that completely fills left lobe of liver which interpreted in favor of hydatid cyst. Histopathologically, the inner surface of the cyst was covered with low grade mucinous epithelium. Ovarian-type stroma was detectable only by immunohistochemistry due to significant bleeding and edema on the wall. The diagnosis of both of our cases was low grade MCN-L. Since cysts were not intact at the time of gross examination, we could not make any comment about surgical margins or total excision. MCN-L is a tumor that creates difficulty in presurgical differential diagnosis because of its rarity and lack of specific radiologic features. Although the prognosis is excellent as a result of total excision in the benign group, relapses have also been reported.
摘要：
肝脏粘液性囊性肿瘤（MCN-L）是一种罕见的肿瘤，占所有肝囊肿的不到5％。尽管它们由于生长缓慢而在放射学和临床上被认为是“良性囊肿”，他们被认为是恶性的。我们介绍了两个在短时间范围内手术的放射学误诊病例，以提高对这些罕见肿瘤的认识。一名47岁的女性患者在肝脏中检测到58x40毫米的囊性病变，放射学诊断为包虫囊肿。病理检查显示多部位囊肿，囊壁上有低度粘液上皮和卵巢型基质。一名50岁女性患者出现腹胀。影像学检查显示，一个204x140毫米的囊性病变完全充满了肝左叶，这有利于包虫囊肿。组织病理学,囊肿的内表面覆盖有低级黏液上皮。由于壁上明显的出血和水肿，只能通过免疫组织化学检测到卵巢型基质。我们两个病例的诊断均为低度MCN-L。由于在大体检查时囊肿并不完整，我们无法对手术切缘或完全切除发表任何评论.MCN-L是一种肿瘤，由于其罕见且缺乏特定的放射学特征，在术前鉴别诊断中遇到困难。尽管良性组完全切除后预后良好，复发也有报道。
