PDF(Pubmed)
Abstract：
A 45-year-old woman presented with right hip pain for a month. Imaging results revealed that the left peritoneal mass was accompanied by metastases of the right sciatic branch, lung, and retroperitoneal lymph nodes. A biopsy of the left peritoneal mass was performed. The pathological morphology demonstrated clear cell adenocarcinoma. Immunohistochemical staining revealed a positive expression of keratin7 and PAX8 and a negative expression of keratin20, GCDFP-15, ER, PR, WT1, CDX2, villin, TTF-1, napsin-A, vimentin, calretinin, and GATA3. Finally, the diagnosis of primary retroperitoneal müllerian adenocarcinoma (PRMA) was confirmed. PRMA is a very rare type of primary retroperitoneal tumor. PRMA should be considered for the retroperitoneal mass.
摘要：
一名45岁的女性出现右髋部疼痛一个月。影像学结果显示，左侧腹膜肿块伴有右侧坐骨神经支转移，肺，和腹膜后淋巴结.对左腹膜肿块进行活检。病理形态学表现为透明细胞腺癌。免疫组织化学染色显示keratin7和PAX8的阳性表达和keratin20，GCDFP-15，ER的阴性表达。PR,WT1,CDX2,绒毛,TTF-1,napsin-A,波形蛋白,calretinin,GATA3最后,诊断为原发性腹膜后苗勒氏腺癌(PRMA).PRMA是一种非常罕见的原发性腹膜后肿瘤。腹膜后肿块应考虑PRMA。
