PDF(Pubmed)
Abstract：
UNASSIGNED: Univentricular heart disease is a relatively rare condition that affects infants, with a prevalence ranging from 0.05 to 0.1 per 1000 live births. It is characterized by an abnormality in the structure of the heart, specifically the presence of only one main pumping chamber (ventricle) instead of the usual two.
UNASSIGNED: In this particular case, a newborn male was diagnosed with double-inlet left ventricle (DILV), a specific form of univentricular heart disease. Following his birth, he exhibited symptoms of central cyanosis (a bluish tint to the skin due to poor oxygenation) and difficulties with breastfeeding. Clinical evaluation, along with a heart ultrasound, confirmed the need for palliative surgery. At the age of 6 months, the patient is scheduled to undergo the Glenn procedure, a surgical intervention that aims to redirect blood flow to the lungs and improve oxygenation.
UNASSIGNED: Given the complexity of double-inlet single ventricle anomalies, there are multiple differential diagnoses that need to be considered for accurate diagnosis, including conditions such as tricuspid atresia, large ventricular septal defect and corrected transposition of the great arteries with ventricular septal defect.
UNASSIGNED: Early intervention in the immediate postnatal period plays a crucial role in improving survival rates and reducing long-term complications. It is, therefore, essential to continue researching and refining treatment approaches.
UNASSIGNED: In this particular case, a newborn male was diagnosed with double-inlet left ventricle (DILV), a specific form of univentricular heart disease. Following his birth, he exhibited symptoms of central cyanosis (a bluish tint to the skin due to poor oxygenation) and difficulties with breastfeeding. Clinical evaluation, along with a heart ultrasound, confirmed the need for palliative surgery. At the age of 6 months, the patient is scheduled to undergo the Glenn procedure, a surgical intervention that aims to redirect blood flow to the lungs and improve oxygenation.
UNASSIGNED: Given the complexity of double-inlet single ventricle anomalies, there are multiple differential diagnoses that need to be considered for accurate diagnosis, including conditions such as tricuspid atresia, large ventricular septal defect and corrected transposition of the great arteries with ventricular septal defect.
UNASSIGNED: Early intervention in the immediate postnatal period plays a crucial role in improving survival rates and reducing long-term complications. It is, therefore, essential to continue researching and refining treatment approaches.
摘要：
■单室心脏疾病是影响婴儿的一种相对罕见的疾病，患病率为每1000名活产儿0.05至0.1。它的特征是心脏结构异常，特别是只有一个主泵室（心室）的存在，而不是通常的两个。
■在这种特殊情况下，一名新生男性被诊断为左心室双入口（DILV），一种特殊形式的单室心脏病。在他出生之后,他表现出中枢紫癜症状（由于氧合不良，皮肤呈蓝色）和母乳喂养困难。临床评价,还有心脏超声检查，证实了姑息性手术的必要性。在6个月大的时候，病人计划接受Glenn手术,一种旨在将血流重新导向肺部并改善氧合的外科手术。
■考虑到双入口单心室异常的复杂性，为了准确诊断，需要考虑多种鉴别诊断，包括三尖瓣闭锁等条件，巨大的室间隔缺损和校正的大动脉转位伴室间隔缺损。
■产后早期干预在提高生存率和减少长期并发症方面起着至关重要的作用。是的,因此,继续研究和完善治疗方法至关重要。
■在这种特殊情况下，一名新生男性被诊断为左心室双入口（DILV），一种特殊形式的单室心脏病。在他出生之后,他表现出中枢紫癜症状（由于氧合不良，皮肤呈蓝色）和母乳喂养困难。临床评价,还有心脏超声检查，证实了姑息性手术的必要性。在6个月大的时候，病人计划接受Glenn手术,一种旨在将血流重新导向肺部并改善氧合的外科手术。
■考虑到双入口单心室异常的复杂性，为了准确诊断，需要考虑多种鉴别诊断，包括三尖瓣闭锁等条件，巨大的室间隔缺损和校正的大动脉转位伴室间隔缺损。
■产后早期干预在提高生存率和减少长期并发症方面起着至关重要的作用。是的,因此,继续研究和完善治疗方法至关重要。
