Cranial hypertrophic pachymeningitis with myelodysplastic syndrome.

颅骨肥厚性硬脑膜炎伴骨髓增生异常综合征。

• 影响指数: 3.776
• 发表时间: 2024 Jun 30
• 来源期刊: Heliyon
• DOI: 10.1016/j.heliyon.2024.e32973
• PMID: 38988571
• 文章类型: Case Reports
• 作者列表: Kikuchi S,Hayashi T,Nitta H,Kamihara Y,Wada A,Minemura T,Nabe Y,Murakami J,Nakatsuji Y,Sato T

关键词: Hypertrophic pachymeningitis; Myelodysplastic syndrome; Steroids therapy

Abstract

Hypertrophic pachymeningitis (HP) is a rare inflammatory disease characterized by thickening of the dura mater. HP develops with several inflammatory diseases. Antineutrophil cytoplasmic antibody (ANCA)-associated vasculitis and IgG4 related disease are reported as 2 major causes. With hematologic diseases, only 3 cases have been reported. We report the case of myelodysplastic syndrome (MDS) developing HP. Our case provides a thought-provoking hypothesis regarding the potential relationship between MDS and HP.

摘要

肥厚性硬脑膜炎（HP）是一种罕见的炎症性疾病，其特征是硬脑膜增厚。HP伴有几种炎性疾病。据报道，抗中性粒细胞胞浆抗体（ANCA）相关血管炎和IgG4相关疾病是2个主要原因。有血液病，仅报告了3例。我们报告一例骨髓增生异常综合征（MDS）发展为HP。我们的案例提供了一个关于MDS和HP之间潜在关系的发人深省的假设。