PDF(Pubmed)
Abstract：
Pulmonary light chain deposition disease is a rare entity characterized by immunoglobulin deposition within the lung parenchyma with pathologic features distinct from pulmonary amyloidosis. Here, the authors present the clinical presentation, associations, and radiologic features of pulmonary light chain deposition disease in a series of 4 patients as well as discuss the distinctions from amyloidosis. The present case series highlights the frequent presence of both cysts and nodules at CT. Clinically, lymphoma and/or autoimmune disease are often associated.
摘要：
肺轻链沉积病是一种罕见的实体，其特征是免疫球蛋白在肺实质内沉积，具有不同于肺淀粉样变性的病理特征。这里,作者介绍了临床表现，协会,4例患者肺轻链沉积病的影像学特征，并讨论其与淀粉样变性的区别。本病例系列强调了CT时囊肿和结节的频繁存在。临床上,淋巴瘤和/或自身免疫性疾病通常相关。
