PDF(Pubmed)
Abstract：
Rhabdomyosarcoma is a common soft tissue tumor in children but rare in adults. Alveolar rhabdomyosarcoma represents a subtype of rhabdomyosarcoma, extremely rare in adults, especially within the nasal cavities. Therapeutic protocols for adults are often based on those used in pediatric cases. We present the case of a 56-year-old female patient with a history of breast cancer who developed alveolar rhabdomyosarcoma of the nasal cavity, stage III, managed initially with chemotherapy resulting in partial response. Subsequently, the patient underwent concomitant chemoradiotherapy. The clinical course was marked by local remission with metastatic progression after 18 months. Alveolar rhabdomyosarcoma is uncommon in adults, and its therapeutic management remains non-standardized. However, it is typically based on initial chemotherapy followed by local treatment. Despite therapeutic advances, the prognosis remains poor.
摘要：
横纹肌肉瘤是儿童常见的软组织肿瘤，但在成人中很少见。肺泡横纹肌肉瘤代表横纹肌肉瘤的亚型，在成年人中极为罕见，尤其是在鼻腔内.成人的治疗方案通常基于儿科病例中使用的方案。我们介绍了一个有乳腺癌病史的56岁女性患者的病例，该患者发展为鼻腔的肺泡横纹肌肉瘤，第三阶段,最初用化疗管理，导致部分反应。随后，患者接受同步放化疗.临床过程以18个月后局部缓解和转移性进展为标志。肺泡横纹肌肉瘤在成人中并不常见，其治疗管理仍不规范。然而,它通常是基于最初的化疗，然后是局部治疗。尽管治疗取得了进展，预后仍然很差。
