PDF(Pubmed)
Abstract：
Moyamoya disease (MMD) is a chronic cerebro-vasculopathy that is extremely rare in the pediatric population. The main characteristic feature is the progressive stenosis in the internal carotid artery with or without the involvement of its main branches in the circle of Willis leading to ischemic stroke. Patients have clinical manifestations related to cerebral ischemia in the carotid branch territories, such as sensory impairment, hemiparesis, and aphasia/dysarthria. Herein, we report a case of MMD in a six-year-old Emirati female who presented with unusual manifestations of MMD in the form of headache, vomiting, and double vision and was diagnosed with MMD based on a brain MRI with angiography. To our knowledge, this is the first reported case of MMD in the United Arab Emirates.
摘要：
烟雾病（MMD）是一种慢性脑血管疾病，在儿科人群中极为罕见。主要特征是颈内动脉的进行性狭窄，无论威利斯环中的主要分支是否受累，都会导致缺血性中风。患者在颈动脉分支区域有与脑缺血相关的临床表现，如感觉障碍，偏瘫,和失语症/构音障碍。在这里，我们报告了一名6岁的阿联酋女性的MMD病例，她以头痛的形式出现了MMD的异常表现，呕吐,和复视，并根据血管造影的脑部MRI诊断为MMD。据我们所知,这是阿拉伯联合酋长国首例报告的MMD病例.
