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Abstract：
Introduction One of the paths in the investigation of congenital sensorineural hearing loss (CSNHL) is to try to characterize its etiology through the inner ear evaluation using high resolution computer tomography (CT) scans. With minor malformation, it is not always possible for a simple visual inspection to recognize if the structure in the inner ear is normal or not. Objective To verify if measurements of the inner ear are predictive of sensorineural hearing loss (SNHL) and suggest cutoff points of size limits. Methods Retrospective cross-sectional study of inner ear CT scan measurements of 214 patients, 50 with congenital SNHL (CSNHL) and 164 acquired SNHL (ASNHL) (control group). Results In the CSNHL group, central bony island (CBI) were 0.48 mm smaller ( p < 0.001), cochlear nerve aperture was (CNA) 0.10 mm smaller ( p < 0.001), and cochlea height was (CH) 0.15 mm smaller ( p < 0.001). Vestibular aqueduct (VA) and cochlea width (CW) were similar between groups (0.70 vs 0.72, p = 0.19, and 7.20 vs 7.15 p = 0.23). The predictive cutoff points for CSNHL were CBI = 3.6 mm, CAN = 1.4 mm, CH = 3.4 mm, CW = 7.0 mm, and VA = 0.9 mm. Conclusion Congenital sensorineural hearing loss determined a decrease in CBI, opening of the cochlear nerve (OCN), and CW. Thus, these measures, at the cutoff points indicated, should make us aware of the diagnosis of congenital hearing loss.
摘要：
介绍先天性感觉神经性听力损失（CSNHL）研究的途径之一是尝试通过使用高分辨率计算机断层扫描（CT）扫描进行内耳评估来表征其病因。有轻微畸形，简单的视觉检查并不总是可以识别内耳的结构是否正常。目的验证内耳的测量是否可以预测感觉神经性听力损失（SNHL），并建议尺寸限制的截止点。方法回顾性横断面研究214例患者的内耳CT扫描测量,50例先天性SNHL（CSNHL）和164例获得性SNHL（ASNHL）（对照组）。结果在CSNHL组中，中央骨岛（CBI）小0.48毫米（p<0.001），耳蜗神经孔径（CNA）小0.10mm（p<0.001），耳蜗高度（CH）小0.15mm（p<0.001）。各组前庭水管（VA）和耳蜗宽度（CW）相似（0.70vs0.72，p=0.19，7.20vs7.15p=0.23）。CSNHL的预测截止点为CBI=3.6mm，CAN=1.4mm,CH=3.4mm,CW=7.0mm,和VA=0.9毫米。结论先天性感觉神经性听力损失决定了CBI的减少，耳蜗神经（OCN）的开放，和CW。因此，这些措施,在所示的截止点，应该让我们了解先天性耳聋的诊断。
