PDF(Pubmed)
Abstract：
BACKGROUND: Aortic atresia with ventricular septal defect is a very rare congenital cardiac anomaly, especially in combination with aortic arch interruption. It is always challenging to choose the optimal treatment tactics for such patients. One of the possible types of intervention is the Yasui procedure. There are only 19 reported cases in the literature of aortic atresia with interruption of the aortic arch type B or C, and not a single clinical case of type A.
METHODS: The proband was a 2-day-old boy with diagnosis: aortic atresia with a ventricular septal defect and interruption of the aortic arch type B. The child underwent a Yasui procedure without serious postoperative complications and with good long-term result.
CONCLUSIONS: The Yasui procedure in patients with aortic atresia and interrupted aortic arch can be performed with minimal complications, even in low-weight patients.
METHODS: The proband was a 2-day-old boy with diagnosis: aortic atresia with a ventricular septal defect and interruption of the aortic arch type B. The child underwent a Yasui procedure without serious postoperative complications and with good long-term result.
CONCLUSIONS: The Yasui procedure in patients with aortic atresia and interrupted aortic arch can be performed with minimal complications, even in low-weight patients.
摘要：
背景：主动脉瓣闭锁伴室间隔缺损是一种非常罕见的先天性心脏异常，尤其是与主动脉弓中断相结合。为此类患者选择最佳治疗策略总是具有挑战性。可能的干预类型之一是Yasui程序。文献中仅有19例主动脉弓闭锁伴主动脉弓B型或C型中断，
方法：先证者是一个2天大的男孩，诊断为：主动脉闭锁伴室间隔缺损和主动脉弓B型中断。该孩子接受了Yasui手术，没有严重的术后并发症，长期效果良好。
结论：对主动脉闭锁和主动脉弓中断的患者进行Yasui手术，并发症少，即使是低体重患者。
方法：先证者是一个2天大的男孩，诊断为：主动脉闭锁伴室间隔缺损和主动脉弓B型中断。该孩子接受了Yasui手术，没有严重的术后并发症，长期效果良好。
结论：对主动脉闭锁和主动脉弓中断的患者进行Yasui手术，并发症少，即使是低体重患者。
