Abstract：
A woman in her 70s was seen in the gynaecology outpatient clinic with a swelling on the right side of the vulva. Surgical excision of the lesion revealed unexpectedly an extensive ductal carcinoma in situ with a focus of a grade 2 invasive ductal carcinoma arising in extramammary breast tissue of the vulva. Postoperative staging studies showed normal breasts, with no evidence of disease elsewhere. The patient underwent a wider excision of the right vulva and sentinel node biopsy of the right inguinal region, which revealed no further disease. The patient is currently taking adjuvant hormonal therapy and has remained disease free at 2-year follow-up. This case underscores the importance of considering rare presentations of vulvar malignancies and the necessity for a multidisciplinary approach in managing such cases.
摘要：
在妇科门诊看到一名70多岁的妇女，外阴右侧肿胀。病变的手术切除意外地发现了广泛的原位导管癌，病灶为2级浸润性导管癌，起源于外阴的乳腺组织。术后分期研究显示乳房正常,在其他地方没有疾病的证据。患者接受了右外阴广泛切除术和右腹股沟区前哨淋巴结活检，这表明没有进一步的疾病。患者目前正在接受辅助激素治疗，并在2年的随访中保持无病。此病例强调了考虑罕见外阴恶性肿瘤的重要性，以及在处理此类病例时采用多学科方法的必要性。
