Abstract：
A 23-year-old female symptomatic with unilateral proptosis with superior globe displacement and hypertropia was found to have a multiloculated cystic lesion with bony lining arising from the inferomedial orbit. The adjacent maxillary sinus was markedly smaller on the affected side, with no defect of the wall on radiographic or intraoperative examination. Surgical excision and histological analysis of the lesion demonstrated an orbital respiratory epithelial cyst. A literature review of congenital orbital respiratory epithelial cysts is presented. To our knowledge, this is the first published case of choristomatous orbital respiratory epithelial cyst associated with ossification, and a primary or secondary anomaly of the adjacent sinus without bony defect.
摘要：
一名23岁的女性症状为单侧眼球突出，并伴有上眼球移位和高斜视，被发现患有多部位囊性病变，由下眼眶引起骨膜。相邻的上颌窦在患侧明显较小，影像学或术中检查壁无缺损。手术切除和病变的组织学分析表明眼眶呼吸道上皮囊肿。本文对先天性眼眶呼吸道上皮囊肿进行了文献综述。据我们所知,这是第一例与骨化相关的脉络膜性眼眶呼吸道上皮囊肿，相邻窦的原发性或继发性异常，无骨缺损。
