Abstract：
Congenital diaphragmatic hernia (CDH) is a congenital anomaly involving the herniation of intra-abdominal contents into the thoracic cavity. Hepatopulmonary fusion (HPF), an exceedingly rare subtype mainly associated with right-sided CDH, presents unique diagnostic and therapeutic challenges. This case report describes a male infant with right-sided CDH complicated by HPF. The intricate anatomical anomaly involved the fusion of the right lung to the liver, posing challenges during surgical separation. The patient experienced postoperative complications, including prolonged ventilation, tracheostomy and pulmonary issues, which led to a prolonged hospital stay. Intraoperative challenges stem from the absence of demarcation between lung and liver tissues and abnormal vascular structures. In summary, managing HPF in right-sided CDH necessitates a customised, multidisciplinary approach to optimise patient outcomes, highlighting the need for ongoing research to refine understanding and treatment strategies.
摘要：
先天性膈疝（CDH）是一种先天性异常，涉及腹内内容物疝到胸腔。肝肺融合(HPF),一种极其罕见的亚型，主要与右侧CDH相关，提出了独特的诊断和治疗挑战。该病例报告描述了一名患有右侧CDH并伴有HPF的男婴。复杂的解剖异常涉及右肺与肝脏的融合，在手术分离过程中面临挑战。患者出现术后并发症,包括长时间的通风，气管造口术和肺部问题，这导致了长时间的住院。术中挑战源于肺和肝组织之间没有分界以及异常的血管结构。总之,在右侧CDH中管理HPF需要定制的，多学科方法来优化患者的结果，强调需要进行持续的研究，以完善理解和治疗策略。
