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Abstract：
Fat embolism syndrome (FES) is a rather uncommon presentation in sickle cell disease (SCD), most frequently happening in the context of long bone fractures following trauma. On the other hand, nontraumatic scenarios and nonorthopedic injuries have been documented to cause fat embolisms. This article describes the case of an 18-year-old male patient who had a known case of SCD (SS pattern). The patient complained of hip pain, and it was discovered that he had avascular necrosis of the right femoral head. The patient was started on opioid analgesics and started to respond to treatment; however, on the third day of admission, his condition deteriorated, oxygen saturation dropped, and the patient was shifted to the intensive care unit, where he was diagnosed with FES due to avascular necrosis. The patient\'s condition further deteriorated; he could not be saved and succumbed to death within one day. Very rarely has SCD with FES been reported in the literature.
摘要：
脂肪栓塞综合征（FES）是镰状细胞病（SCD）中相当罕见的表现，最常见于创伤后长骨骨折。另一方面,非创伤性情景和非骨科损伤已被证明会导致脂肪栓塞.本文描述了一名18岁男性患者的病例，该患者患有已知的SCD（SS模式）。病人主诉髋部疼痛,结果发现他的右股骨头缺血性坏死。患者开始使用阿片类镇痛药，并开始对治疗有反应；然而，在入学的第三天，他的病情恶化,氧饱和度下降,病人被转移到重症监护室，他因血管坏死被诊断为FES。病人的病情进一步恶化；他无法得救，并在一天内死亡。文献中很少报道SCD伴FES。
