PDF(Pubmed)
Abstract：
UNASSIGNED: Fontan surgery aims to palliate univentricular congenital heart diseases in which biventricular repair is not feasible. A large spectrum of early and late complications has been described in literature. However, pulmonary thromboembolism represents a rare complication in these patients, leading to a scarcity of evidence regarding diagnosis and treatment strategies.
UNASSIGNED: We present a case of a 27-year-old woman born with a complex cyanotic congenital heart disease, namely pulmonary and tricuspid stenosis with subaortic interventricular communication and atrial septal defect, who underwent palliation surgery with Blalock-Taussig shunt, bidirectional Glenn, and extracardiac Fontan. She developed acute respiratory failure and was admitted to the hospital, being diagnosed with bilateral thromboembolism. Since she was haemodynamically stable, initially, a conservative approach was chosen. However, due to no clinical improvement, she subsequently underwent bilateral thromboaspiration with restoration of pulmonary circulation.
UNASSIGNED: Due to the unique Fontan pathophysiology, the possible physiological and clinical implications of pulmonary thromboembolism in this condition are profound. Thus, care and imaging tests in specialized centres are important as the management of these patients is different from those with biventricular physiology.
UNASSIGNED: We present a case of a 27-year-old woman born with a complex cyanotic congenital heart disease, namely pulmonary and tricuspid stenosis with subaortic interventricular communication and atrial septal defect, who underwent palliation surgery with Blalock-Taussig shunt, bidirectional Glenn, and extracardiac Fontan. She developed acute respiratory failure and was admitted to the hospital, being diagnosed with bilateral thromboembolism. Since she was haemodynamically stable, initially, a conservative approach was chosen. However, due to no clinical improvement, she subsequently underwent bilateral thromboaspiration with restoration of pulmonary circulation.
UNASSIGNED: Due to the unique Fontan pathophysiology, the possible physiological and clinical implications of pulmonary thromboembolism in this condition are profound. Thus, care and imaging tests in specialized centres are important as the management of these patients is different from those with biventricular physiology.
摘要：
■Fontan手术旨在缓解双心室修复不可行的单心室先天性心脏病。文献中已经描述了大量的早期和晚期并发症。然而,肺血栓栓塞在这些患者中是一种罕见的并发症，导致缺乏关于诊断和治疗策略的证据。
我们介绍了一例27岁女性出生时患有复杂的紫红色先天性心脏病，即肺动脉和三尖瓣狭窄伴主动脉室间连通和房间隔缺损，他接受了Blalock-Taussig分流术的姑息手术，双向格伦,和心外丰坦。她出现急性呼吸衰竭,住进医院,被诊断为双侧血栓栓塞。因为她的血液动力学稳定，最初,选择了保守的方法。然而,由于没有临床改善，她随后接受了双侧血栓抽吸术,同时恢复了肺循环.
■由于Fontan独特的病理生理学，在这种情况下，肺血栓栓塞症可能的生理和临床意义是深远的。因此，专业中心的护理和影像学检查很重要，因为这些患者的管理不同于双心室生理学患者。
我们介绍了一例27岁女性出生时患有复杂的紫红色先天性心脏病，即肺动脉和三尖瓣狭窄伴主动脉室间连通和房间隔缺损，他接受了Blalock-Taussig分流术的姑息手术，双向格伦,和心外丰坦。她出现急性呼吸衰竭,住进医院,被诊断为双侧血栓栓塞。因为她的血液动力学稳定，最初,选择了保守的方法。然而,由于没有临床改善，她随后接受了双侧血栓抽吸术,同时恢复了肺循环.
■由于Fontan独特的病理生理学，在这种情况下，肺血栓栓塞症可能的生理和临床意义是深远的。因此，专业中心的护理和影像学检查很重要，因为这些患者的管理不同于双心室生理学患者。
