Abstract：
BACKGROUND: Traboulsi syndrome is a sporadic autosomal recessive disorder. Very few cases reported and no surgical treatment has been described.
OBJECTIVE: The purpose of the study was to describe the surgical treatment of a case of Traboulsi syndrome with intercalary staphyloma.
CONCLUSIONS: Traboulsi syndrome[1-3] is a type of spontaneous filtering bleb. The case was of a 31-year-old lady with a flat anterior chamber and large intercalary staphyloma, with a subluxated clear lens. Liberal peritomy was done. The staphyloma was cut and the displaced lens was delivered through it. It was closed with 7-0 vicryl continuous suture. A cross-linked cornea was used after removing the Descemet membrane. It was modified to match the crescentic shape of the limbus by using 11 and 6 mm trephine. Two wedge-shaped defects were created and tissue was excised between them, which were then sutured to increase the arc radius. A peripheral flange at the corneal edge was created. A pocket was created in the host cornea to accommodate the donor corneal flange. The donor cornea was tucked in and the graft was sutured. The sclera was used to suture another side prophylactically, making a 360-degree encirclage. The patient got ambulatory vision postsurgery. The use of the cornea as biological encirclage has not been described previously.
CONCLUSIONS: Using a cross-linked cornea. Creating wedge-shaped defects in crescentic corneal graft to increase arc radius. Use of cornea as encirclage.Link of video:https://youtu.be/T3b5rkvFmlc.
OBJECTIVE: The purpose of the study was to describe the surgical treatment of a case of Traboulsi syndrome with intercalary staphyloma.
CONCLUSIONS: Traboulsi syndrome[1-3] is a type of spontaneous filtering bleb. The case was of a 31-year-old lady with a flat anterior chamber and large intercalary staphyloma, with a subluxated clear lens. Liberal peritomy was done. The staphyloma was cut and the displaced lens was delivered through it. It was closed with 7-0 vicryl continuous suture. A cross-linked cornea was used after removing the Descemet membrane. It was modified to match the crescentic shape of the limbus by using 11 and 6 mm trephine. Two wedge-shaped defects were created and tissue was excised between them, which were then sutured to increase the arc radius. A peripheral flange at the corneal edge was created. A pocket was created in the host cornea to accommodate the donor corneal flange. The donor cornea was tucked in and the graft was sutured. The sclera was used to suture another side prophylactically, making a 360-degree encirclage. The patient got ambulatory vision postsurgery. The use of the cornea as biological encirclage has not been described previously.
CONCLUSIONS: Using a cross-linked cornea. Creating wedge-shaped defects in crescentic corneal graft to increase arc radius. Use of cornea as encirclage.Link of video:https://youtu.be/T3b5rkvFmlc.
摘要：
背景：Traboulsi综合征是一种散发性常染色体隐性遗传疾病。报道的病例很少，没有描述手术治疗。
目的：本研究的目的是描述一例Traboulsi综合征伴cal间葡萄肿的手术治疗。
结论：Traboulsi综合征[1-3]是一种自发性滤过泡。该病例是一名31岁的女士，患有平坦的前房和大的cal间葡萄肿，带有半脱位的透明晶状体。自由主义的peritomy已经完成。切割葡萄肿，并通过它输送移位的晶状体。用7-0vicryl连续缝合线将其封闭。在去除Descemet膜后使用交联的角膜。通过使用11和6mm的环钻对其进行修改以匹配角膜缘的新月形形状。产生了两个楔形缺损，并在它们之间切除了组织，然后缝合以增加圆弧半径。在角膜边缘处形成外围凸缘。在宿主角膜中形成口袋以容纳供体角膜凸缘。将供体角膜塞入并缝合移植物。巩膜用于预防性缝合另一侧，做一个360度的包围.患者术后有动态视力。以前没有描述过角膜作为生物包圈的用途。
结论：使用交联角膜。在新月体角膜移植物中创建楔形缺损以增加圆弧半径。使用角膜作为包围。视频链接：https://youtu.be/T3b5rkvFmlc。
目的：本研究的目的是描述一例Traboulsi综合征伴cal间葡萄肿的手术治疗。
结论：Traboulsi综合征[1-3]是一种自发性滤过泡。该病例是一名31岁的女士，患有平坦的前房和大的cal间葡萄肿，带有半脱位的透明晶状体。自由主义的peritomy已经完成。切割葡萄肿，并通过它输送移位的晶状体。用7-0vicryl连续缝合线将其封闭。在去除Descemet膜后使用交联的角膜。通过使用11和6mm的环钻对其进行修改以匹配角膜缘的新月形形状。产生了两个楔形缺损，并在它们之间切除了组织，然后缝合以增加圆弧半径。在角膜边缘处形成外围凸缘。在宿主角膜中形成口袋以容纳供体角膜凸缘。将供体角膜塞入并缝合移植物。巩膜用于预防性缝合另一侧，做一个360度的包围.患者术后有动态视力。以前没有描述过角膜作为生物包圈的用途。
结论：使用交联角膜。在新月体角膜移植物中创建楔形缺损以增加圆弧半径。使用角膜作为包围。视频链接：https://youtu.be/T3b5rkvFmlc。
