Abstract：
BACKGROUND: Pleomorphic hyalinizing angiectatic tumor (PHAT) is a rare low-grade malignant mesenchymal neoplasm. It commonly occurs in the limbs and trunk, with limited occurrences in the head and neck region. Only five cases of PHAT occurring in the head and neck have been reported in the literature to date. The etiology of PHAT remains unclear. We described a case of nasal cavity PHAT following CARE guidelines.
METHODS: A 32-year-old male with PHAT originating in the nasal cavity recurred after two surgeries. Adjuvant radiotherapy was performed after the third surgery. The patient has been regularly followed up for 36months, and no tumor recurrence or metastasis has been observed.
CONCLUSIONS: PHAT is a rare soft tissue tumor known for its local aggressiveness. Because of a high risk of recurrence, extensive resection should be implemented, possibly completed by radiotherapy if resection cannot be complete because of proximity to at-risk structures.
METHODS: A 32-year-old male with PHAT originating in the nasal cavity recurred after two surgeries. Adjuvant radiotherapy was performed after the third surgery. The patient has been regularly followed up for 36months, and no tumor recurrence or metastasis has been observed.
CONCLUSIONS: PHAT is a rare soft tissue tumor known for its local aggressiveness. Because of a high risk of recurrence, extensive resection should be implemented, possibly completed by radiotherapy if resection cannot be complete because of proximity to at-risk structures.
摘要：
背景：多形性透明血管扩张肿瘤（PHAT）是一种罕见的低度恶性间充质肿瘤。它通常发生在四肢和躯干，在头部和颈部区域的发生率有限。迄今为止，文献中仅报道了5例发生在头颈部的PHAT。PHAT的病因尚不清楚。我们描述了一例遵循CARE指南的鼻腔PHAT病例。
方法：一名来自鼻腔的PHAT的32岁男性在两次手术后复发。第三次手术后进行辅助放疗。患者已定期随访36个月，未观察到肿瘤复发或转移。
结论：PHAT是一种罕见的软组织肿瘤，以其局部侵袭性而闻名。因为复发的风险很高，应实施广泛切除，如果由于靠近危险结构而无法完成切除，则可能通过放射治疗完成。
方法：一名来自鼻腔的PHAT的32岁男性在两次手术后复发。第三次手术后进行辅助放疗。患者已定期随访36个月，未观察到肿瘤复发或转移。
结论：PHAT是一种罕见的软组织肿瘤，以其局部侵袭性而闻名。因为复发的风险很高，应实施广泛切除，如果由于靠近危险结构而无法完成切除，则可能通过放射治疗完成。
