关键词: Purtscher flecken Purtscher-like retinopathy juvenile dermatomyositis pneumonitis

来  源:   DOI:10.3205/oc000237   PDF(Pubmed)

Abstract:
UNASSIGNED: To report a rare case of bilateral Purtscher-like retinopathy (PLR) in a young adult diagnosed with dermatomyositis.
UNASSIGNED: A case report with multi-modal imaging.
UNASSIGNED: A 17-year-old male presented with subacute marked diminution of vision along with arthralgia, weakness of all four limbs and development of multiple rashes around body. Fundus examination revealed bilateral multiple Purtscher flecken, pseudo-cherry red spot, and intra-retinal haemorrhages with cotton wool spots. Systemic and laboratory examinations, magnetic resonance imaging (MRI) and biopsy of tissue confirmed the diagnosis of juvenile dermatomyositis with PLR.
UNASSIGNED: Dermatomyositis, being a rare cause of PLR, should essentially be considered as one of the differentials as timely intervention can alter the course of disease and prove life-saving for the patient.
摘要:
报告一例罕见的双侧Purtscher样视网膜病变(PLR)的年轻成人被诊断为皮肌炎。
多模态成像病例报告。
一名17岁男性表现为亚急性视力明显减退并伴有关节痛,四肢无力和身体周围多发皮疹的发展。眼底检查显示双侧多发性PurtscherFlecken,假樱桃红点,和视网膜内出血与棉绒斑点。系统和实验室检查,磁共振成像(MRI)和组织活检证实PLR诊断为青少年皮肌炎。
皮肌炎,是PLR的罕见原因,基本上应该被认为是区别之一,因为及时的干预可以改变疾病的进程,并证明病人的生命。
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