PDF(Pubmed)
Abstract：
Myofibrosarcoma is a distinct mesenchymal malignancy which commonly occurs in head and neck region. It has a high tendency for local recurrence and distant metastasis. 39-year-old male presented with epistaxis, nasal obstruction and left sided complete loss of vision. He underwent functional endoscopic sinus surgery and guided biopsy. MRI scan showed a lesion epicentred in the left maxillary sinus, superiorly extending into the orbit. He underwent Class 4b maxillectomy with neck dissection, tracheostomy and free flap reconstruction. Histopathological examination yielded final diagnosis as myofibrosarcoma of maxilla. The patient was planned for adjuvant radiotherapy and has been disease free for 3 years.
摘要：
肌纤维肉瘤是一种独特的间充质恶性肿瘤，通常发生在头颈部。具有较高的局部复发和远处转移倾向。39岁男性出现鼻出血,鼻塞和左侧完全丧失视力。他接受了功能性内窥镜鼻窦手术和引导活检。MRI扫描显示左侧上颌窦病灶,向上延伸到轨道上。他接受了4b级上颌骨切除术和颈部清扫术，气管切开和游离皮瓣重建。组织病理学检查最终诊断为上颌骨肌纤维肉瘤。该患者计划接受辅助放疗，并且已经无病3年。
