Abstract:
Solitary fibrous tumors (SFTs) belonging to a distinct group of mesenchymal tumors, was originally described by Klemper and Rabin in the pleura in year 1931. However, it can also be extra-pleural in origin. With tongue being the most common site involved in this region, epiglottis, larynx, thyroid, external auditory canal, lacrimal sac, hypoglossal nerve, parotid gland, sublingual gland, Para pharyngeal space, nasopharynx, scalp, gingiva, orbit and infratemporal fossa as well as paranasal sinuses and nasal cavities can also get involved. But SFTs involving nasal cavities and nasopharynx are quite uncommon, accounting for < 0.1% of all Sino-nasal neoplasms. Until now there have only been 40 cases of nasal SFT reported in literature. We report the case of an extraserosa solitary fibrous tumor arising from the nasal cavity with extension to the sphenoid sinus, a much rarer presentation of its type. Our case report is one of its type, emphasizing the need conducting further studies on the nature and management of the disease.
摘要:
孤立性纤维性肿瘤(SFT)属于一组不同的间充质肿瘤,最初由Klemper和Rabin于1931年在胸膜中描述。然而,它也可以是胸膜外来源。舌头是这个地区最常见的部位,会厌,喉部,甲状腺,外耳道,泪囊,舌下神经,腮腺,舌下腺,咽旁空间,鼻咽部,头皮,牙龈,眼眶和颞下窝以及鼻旁窦和鼻腔也可能受累。但是涉及鼻腔和鼻咽的SFT并不常见,占所有鼻部肿瘤的<0.1%。到目前为止,文献报道的鼻SFT只有40例。我们报告了从鼻腔延伸到蝶窦的血管外孤立性纤维瘤的病例,这种类型的更罕见的介绍。我们的病例报告是其中一种,强调需要对疾病的性质和管理进行进一步研究。