PDF(Pubmed)
Abstract：
In a rare condition known as vaginal agenesis, the uterus (womb) may develop only partially or not at all, while the vagina fails to develop altogether. It is common to diagnose vaginal agenesis, when a female does not start menstruation at puberty. This is a prenatal disorder that may also be linked to bone or kidney issues. Mullerian agenesis, Mullerian aplasia, and Mayer-Rokitansky-Kuster-Hauser (MRKH) syndrome are other names for the illness. Treatment modalities encompass surgical and nonsurgical interventions, including the utilization of prefabricated or customized vaginal stents for neovagina reconstruction and maintenance. This case report describes the development of a neovagina in a 27-year-old female diagnosed with vaginal agenesis, a characteristic of MRKH syndrome. A customized clear acrylic stent, designed to provide a resilient surface, serves as a straightforward and cost-efficient alternative for managing this condition. Significantly, it enhances patient\'s compliance and comfort during treatment, addressing both the physical and psychological ramifications of this congenital anomaly. This customized vaginal stent not only provides a practical solution but also contributes to enhancing the quality of life for individuals grappling with vaginal agenesis, thereby offering a promising avenue for addressing the multifaceted challenges associated with this condition.
摘要：
在一种称为阴道发育不全的罕见疾病中，子宫（子宫）可能仅部分发育或根本不发育，而阴道完全不能发育。诊断阴道发育不全是很常见的，当女性在青春期没有开始月经时。这是一种产前疾病，也可能与骨骼或肾脏问题有关。穆勒氏症,Mullerian发育不全,Mayer-Rokitansky-Kuster-Hauser（MRKH）综合征是该疾病的其他名称。治疗方式包括手术和非手术干预，包括使用预制或定制的阴道支架进行新阴道重建和维护。该病例报告描述了一名被诊断为阴道发育不全的27岁女性的新阴道发育，MRKH综合征的特征。定制的透明丙烯酸支架，旨在提供弹性表面，作为管理这种情况的直接和成本有效的替代方案。重要的是,它增强了患者在治疗期间的依从性和舒适度，解决这种先天性异常的生理和心理后果。这种定制的阴道支架不仅提供了实用的解决方案，而且有助于提高患有阴道发育不全的个人的生活质量，从而为解决与这种情况相关的多方面挑战提供了一个有希望的途径。
