Abstract：
UNASSIGNED: A 17-year-old boy with Von Hippel-Lindau syndrome presented with hypertension, raised plasma catecholamines, and MRI findings of a new pancreatic tail lesion and 2 stable right adrenal lesions concerning for functional neuroendocrine tumors. A 68 Ga-DOTATATE PET/CT demonstrated intense tracer avidity within the pancreatic lesion with minimal uptake in the adrenal lesions. Conversely, a 123 I-MIBG SPECT/CT study demonstrated high-grade tracer uptake within the adrenal lesions, with no significant uptake appreciated in the pancreatic lesion. The adrenal lesions were resected, and pathology was consistent with pheochromocytoma. Plasma catecholamines returned to within the normal range and hypertension resolved.
摘要：
■一名17岁男孩，患有VonHippel-Lindau综合征，并伴有高血压，提高血浆儿茶酚胺，1个新的胰尾病变和2个稳定的右肾上腺病变的MRI表现为功能性神经内分泌肿瘤。68Ga-DOTATATEPET/CT在胰腺病变内显示出强烈的示踪剂亲和力，而在肾上腺病变中的摄取最小。相反，123I-MIBGSPECT/CT研究显示肾上腺病变内的高度示踪剂摄取，胰腺病变没有明显的摄取。切除肾上腺病变,病理符合嗜铬细胞瘤。血浆儿茶酚胺恢复到正常范围内，高血压消退。
