PDF(Pubmed)
Abstract：
BACKGROUND: Darier Ferrand Dermatofibrosarcoma (DFSP) is a rare skin tumor, characterized by its local aggressivity and high potential of recurrence. It affects mainly young and middle-aged adults. Its location in the head and neck region represents nearly 12.5 % of all DFSP.
METHODS: We report a rare case of a 68-year-old patient who was treated for a DFSP of the cheek\'s lower part with reconstruction using a pectoralis major musculocutaneous flap. The postoperative course was uneventful and the aesthetic result was good.
CONCLUSIONS: DFSP is a tumor of intermediate malignancy. Its optimal management is based on complete surgical excision requiring various reconstruction procedures for large defects. The treatment of unresectable lesions remains difficult despite the targeted therapies proposed and the improvement of radiotherapy techniques.
CONCLUSIONS: The ideal management of a DFSP is based on surgical excision passing largely in healthy tissues. This situation requires early diagnosis and is the guarantee of disease-free survival without major sequelae in head and neck locations.
METHODS: We report a rare case of a 68-year-old patient who was treated for a DFSP of the cheek\'s lower part with reconstruction using a pectoralis major musculocutaneous flap. The postoperative course was uneventful and the aesthetic result was good.
CONCLUSIONS: DFSP is a tumor of intermediate malignancy. Its optimal management is based on complete surgical excision requiring various reconstruction procedures for large defects. The treatment of unresectable lesions remains difficult despite the targeted therapies proposed and the improvement of radiotherapy techniques.
CONCLUSIONS: The ideal management of a DFSP is based on surgical excision passing largely in healthy tissues. This situation requires early diagnosis and is the guarantee of disease-free survival without major sequelae in head and neck locations.
摘要：
背景：DarierFerrand皮肤纤维肉瘤（DFSP）是一种罕见的皮肤肿瘤，其特点是局部侵袭性和高复发潜力。它主要影响年轻人和中年人。其在头部和颈部区域的位置占所有DFSP的近12.5%。
方法：我们报告了一例罕见的68岁患者，该患者接受了使用胸大肌肌皮瓣重建脸颊下部的DFSP治疗。术后过程顺利，美学效果良好。
结论：DFSP是一种中度恶性肿瘤。其最佳管理基于完整的手术切除，需要对大型缺陷进行各种重建程序。尽管提出了靶向治疗和放射治疗技术的改进，但无法切除的病变的治疗仍然很困难。
结论：DFSP的理想管理是基于在健康组织中进行的手术切除。这种情况需要早期诊断，并且是无病生存的保证，而在头颈部位置没有重大后遗症。
方法：我们报告了一例罕见的68岁患者，该患者接受了使用胸大肌肌皮瓣重建脸颊下部的DFSP治疗。术后过程顺利，美学效果良好。
结论：DFSP是一种中度恶性肿瘤。其最佳管理基于完整的手术切除，需要对大型缺陷进行各种重建程序。尽管提出了靶向治疗和放射治疗技术的改进，但无法切除的病变的治疗仍然很困难。
结论：DFSP的理想管理是基于在健康组织中进行的手术切除。这种情况需要早期诊断，并且是无病生存的保证，而在头颈部位置没有重大后遗症。
