PDF(Pubmed)
Abstract：
BACKGROUND: Crouzon syndrome is an extremely rare craniofacial dysplasia, which is mainly caused by the early ossification and closure of the coronal suture of the skull. Craniofacial deformities can cause stenosis of the nasal cavity and posterior nasal meatus, resulting in sleep apnea.
METHODS: A 9-year-old boy with sleep snoring for 6 years, progressive aggravation in the past 1 month and accompanied by apnea during sleep.
METHODS: This case was diagnosed with Crouzon syndrome complicated with severe obstructive sleep apnea and severe hypoxemia.
METHODS: After adenoidectomy, he was admitted to the pediatric intensive care unit with ventilator-assisted respiration. During this period, the blood oxygen saturation fluctuated greatly. After trying to extubate, the blood oxygen was difficult to maintain and had to be intubated again. After active treatment, extubation was successful.
RESULTS: The wound of nasopharynx recovered well and the sleep state was significantly improved 3 months postoperation.
CONCLUSIONS: It is suggested that the time of ventilator-assisted breathing should be prolonged and the perioperative airway management should be strengthened in order to reduce the risk of postoperative complications.
METHODS: A 9-year-old boy with sleep snoring for 6 years, progressive aggravation in the past 1 month and accompanied by apnea during sleep.
METHODS: This case was diagnosed with Crouzon syndrome complicated with severe obstructive sleep apnea and severe hypoxemia.
METHODS: After adenoidectomy, he was admitted to the pediatric intensive care unit with ventilator-assisted respiration. During this period, the blood oxygen saturation fluctuated greatly. After trying to extubate, the blood oxygen was difficult to maintain and had to be intubated again. After active treatment, extubation was successful.
RESULTS: The wound of nasopharynx recovered well and the sleep state was significantly improved 3 months postoperation.
CONCLUSIONS: It is suggested that the time of ventilator-assisted breathing should be prolonged and the perioperative airway management should be strengthened in order to reduce the risk of postoperative complications.
摘要：
背景：克鲁松综合征是一种极其罕见的颅面发育不良，这主要是由于颅骨冠状缝的早期骨化和闭合引起的。颅面畸形可导致鼻腔和后鼻道狭窄，导致睡眠呼吸暂停。
方法：一个9岁的男孩，睡眠打鼾了6年，在过去的1个月中逐渐加重，并伴有睡眠中的呼吸暂停。
方法：本病例诊断为克鲁松综合征合并重度阻塞性睡眠呼吸暂停和重度低氧血症。
方法：腺样体切除术后，他被送进儿科重症监护室，接受呼吸机辅助呼吸。在此期间,血氧饱和度波动较大。试图拔管后，血氧难以维持，必须再次插管。积极治疗后,拔管成功。
结果：术后3个月鼻咽部创面恢复良好，睡眠状态明显改善。
结论：建议延长呼吸机辅助呼吸时间，加强围手术期气道管理，以降低术后并发症的发生风险。
方法：一个9岁的男孩，睡眠打鼾了6年，在过去的1个月中逐渐加重，并伴有睡眠中的呼吸暂停。
方法：本病例诊断为克鲁松综合征合并重度阻塞性睡眠呼吸暂停和重度低氧血症。
方法：腺样体切除术后，他被送进儿科重症监护室，接受呼吸机辅助呼吸。在此期间,血氧饱和度波动较大。试图拔管后，血氧难以维持，必须再次插管。积极治疗后,拔管成功。
结果：术后3个月鼻咽部创面恢复良好，睡眠状态明显改善。
结论：建议延长呼吸机辅助呼吸时间，加强围手术期气道管理，以降低术后并发症的发生风险。
