PDF(Pubmed)
Abstract：
Pheochromocytomas are rare tumors that present a challenge for surgical and anesthetic management due to their ability to produce significant amounts of catecholamines. This case report highlights the successful management of a 49-year-old woman simultaneously diagnosed with neurofibromatosis type 1, pheochromocytoma, and breast cancer. A key decision by the multidisciplinary team involving endocrinology, general surgery, senology, intensive care, and anesthesiology was to prioritize breast cancer surgery over pheochromocytoma resection. This decision considered the potential for improved prognosis and the need to minimize chemotherapy dosage. The case emphasizes the importance of thorough perioperative preparation, including assessing end-organ damage and optimizing medical therapy. Intraoperative management effectively navigated periods prone to catecholamine release, and postoperative care was closely monitored. This case demonstrates that with meticulous planning, a multidisciplinary approach, and a precise anesthetic strategy, safe anesthesia is achievable for patients with pheochromocytoma undergoing major elective surgeries other than pheochromocytoma resection, adding valuable knowledge to a scarcely documented clinical area.
摘要：
嗜铬细胞瘤是罕见的肿瘤，由于其产生大量儿茶酚胺的能力，对手术和麻醉管理提出了挑战。该病例报告强调了一名49岁女性同时诊断为1型神经纤维瘤，嗜铬细胞瘤的成功治疗。和乳腺癌。涉及内分泌学的多学科团队的关键决定，普外科,Senology,重症监护,麻醉学将乳腺癌手术优先于嗜铬细胞瘤切除术。该决定考虑了改善预后的可能性以及最小化化疗剂量的需要。该病例强调了彻底的围手术期准备的重要性，包括评估终末器官损伤和优化药物治疗。术中管理有效地度过了儿茶酚胺释放的易发时期，术后护理密切监测。这个案例表明，经过精心的计划，多学科方法，和精确的麻醉策略，对于接受嗜铬细胞瘤切除术以外的主要选择性手术的嗜铬细胞瘤患者，可以实现安全的麻醉，为几乎没有记录的临床领域增加有价值的知识。
