PDF(Pubmed)
Abstract：
UNASSIGNED: Proboscis lateralis (PL) is a rare congenital malformation of the craniofacial structure. On the basis of 34 reported cases, Boo-Chai developed the first classification system in 1985 based on commonly associated anomalies of the eyes, palate, and lips. Sinonasal deformity is the most prevalent systemic abnormality associated with PL, accounting for 87.9%, and concomitant ocular anomalies account for 44-70%.
UNASSIGNED: We report a case of PL in a 20-month-old female patient with a mass in the left medial canthal area, and ipsilateral symptomatic epiphora. The removal of the proboscis at 4 months without the reconstruction of the nasolacrimal duct resulted in secondary sequelae that lasted 16 months. A second operation by a multidisciplinary team released the pressure on the lacrimal sac and reconstructed the lacrimal system. External dacryocystorhinostomy (DCR) is performed through the original external incision aided by nasal endoscopic examination. The bony passage between the nasal cavity and the lacrimal sac was reconstructed, and nasal endoscopy revealed a wide opening in the nasal cavity of at least 6 mm. Follow ups ensured a patent nasal airway, without complications.
UNASSIGNED: It is instructive to learn from this case that treatment plans for PL should consider associated ocular anomalies and lacrimal drainage reconstruction, following a comprehensive and multidisciplinary approach.
UNASSIGNED: We report a case of PL in a 20-month-old female patient with a mass in the left medial canthal area, and ipsilateral symptomatic epiphora. The removal of the proboscis at 4 months without the reconstruction of the nasolacrimal duct resulted in secondary sequelae that lasted 16 months. A second operation by a multidisciplinary team released the pressure on the lacrimal sac and reconstructed the lacrimal system. External dacryocystorhinostomy (DCR) is performed through the original external incision aided by nasal endoscopic examination. The bony passage between the nasal cavity and the lacrimal sac was reconstructed, and nasal endoscopy revealed a wide opening in the nasal cavity of at least 6 mm. Follow ups ensured a patent nasal airway, without complications.
UNASSIGNED: It is instructive to learn from this case that treatment plans for PL should consider associated ocular anomalies and lacrimal drainage reconstruction, following a comprehensive and multidisciplinary approach.
摘要：
■长鼻外侧肌（PL）是一种罕见的颅面结构先天性畸形。根据报告的34起案件，Boo-Chai在1985年基于常见的眼睛异常开发了第一个分类系统，腭,和嘴唇。鼻腔鼻窦畸形是与PL相关的最常见的系统性异常，占87.9%，和伴随的眼部异常占44-70％。
■我们报告了一例20个月大的女性患者的PL，其左内侧can区肿块，和同侧有症状的溢唇。在没有重建鼻泪管的情况下，在4个月时切除了长鼻，导致了持续16个月的继发性后遗症。多学科小组进行的第二次手术释放了泪囊的压力，并重建了泪道系统。外部泪囊鼻腔吻合术（DCR）是通过鼻内窥镜检查辅助的原始外部切口进行的。重建鼻腔和泪囊之间的骨通道，和鼻内窥镜检查显示鼻腔中至少6毫米的宽开口。随访确保鼻腔气道通畅，没有并发症。
■从这种情况下了解到，PL的治疗计划应考虑相关的眼部异常和泪道引流重建，遵循全面和多学科的方法。
■我们报告了一例20个月大的女性患者的PL，其左内侧can区肿块，和同侧有症状的溢唇。在没有重建鼻泪管的情况下，在4个月时切除了长鼻，导致了持续16个月的继发性后遗症。多学科小组进行的第二次手术释放了泪囊的压力，并重建了泪道系统。外部泪囊鼻腔吻合术（DCR）是通过鼻内窥镜检查辅助的原始外部切口进行的。重建鼻腔和泪囊之间的骨通道，和鼻内窥镜检查显示鼻腔中至少6毫米的宽开口。随访确保鼻腔气道通畅，没有并发症。
■从这种情况下了解到，PL的治疗计划应考虑相关的眼部异常和泪道引流重建，遵循全面和多学科的方法。
