关键词: Paediatric oncology Radiology Urological surgery

Mesh : Female Humans Magnetic Resonance Imaging Rhabdomyosarcoma, Embryonal / pathology diagnosis diagnostic imaging surgery Ultrasonography Urinary Bladder Neoplasms / diagnostic imaging pathology Vaginal Neoplasms / pathology diagnostic imaging surgery diagnosis Child, Preschool

来  源:   DOI:10.1136/bcr-2023-259549

Abstract:
Rhabdomyosarcomas are the most common soft-tissue sarcomas, found usually in the younger age group. Histologically, they are subdivided into embryonal, alveolar, pleomorphic and not otherwise specified. They have a heterogenous appearance on imaging with few additional characteristic features based on the subtype. Botryoid variant of embryonal rhabdomyosarcoma commonly involves the genitourinary and the biliary system. They can be multifocal. Most of these lesions have a heterogenous appearance on imaging with areas of necrosis and haemorrhage. On ultrasound, they are polypoidal with cystic areas and are vascular. The lesions are hyperintense on T2 sequences, isointense to the skeletal muscle on T1 sequences and show heterogenous enhancement. Surgery is the mainstay of treatment along with radiotherapy or chemotherapy depending on the site and the stage of the tumour. We report a case of botryoid variant of rhabdomyosarcoma involving the vagina and the urinary bladder.
摘要:
横纹肌肉瘤是最常见的软组织肉瘤,通常在较年轻的年龄组中发现。组织学上,它们被细分为胚胎,肺泡,多态且未另作说明。它们在成像时具有异质外观,几乎没有基于亚型的其他特征。胚胎性横纹肌肉瘤的Botryoid变体通常涉及泌尿生殖系统和胆道系统。它们可以是多焦点的。这些病变中的大多数在成像上具有不均匀的外观,具有坏死和出血的区域。在超声波上,它们是息肉状的囊性区域,是血管。病变在T2序列上是高强度的,与T1序列上的骨骼肌呈等强度,并显示出异质性增强。根据肿瘤的部位和阶段,手术是放疗或化疗的主要治疗手段。我们报告了一例涉及阴道和膀胱的横纹肌肉瘤的肉毒杆菌变体。
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