Simultaneous repair of diaphragmatic hernia and ventricular septal defect with postoperative complication in a Down syndrome child.

唐氏综合征患儿同时修复膈疝和室间隔缺损并伴有术后并发症。

• 发表时间: 2024 Jun
• 来源期刊: J Surg Case Rep
• DOI: 10.1093/jscr/rjae301
• PMID: 38832060
• 文章类型: Case Reports
• 作者列表: Almutairi MA,Sultan AF,Alariefy AA,Alzahrani NA,Baghaffar AH,Al-Radi OO

关键词: Down syndrome; Morgagni hernia; VSD; congenital; ventricular septal defect

Abstract

Morgagni hernia (MH) is a rare form of congenital diaphragmatic hernia, typically occurring predominantly on the right side and exhibiting a higher prevalence in females. Usually diagnosed incidentally, MH may coexist with congenital heart defects, chest wall abnormalities and certain genetic syndromes such as Down syndrome. A 4-year-old boy with Down syndrome underwent simultaneous repair of MH and closure of a ventricular septal defect (VSD). A vertical midline sternotomy was performed, and the VSD was repaired using the right atrium approach. Subsequently, MH repair was conducted. Three weeks after the surgery, this patient developed a complete heart block, which lead to the implantation of a VVI pacemaker.

摘要

Morgagni疝（MH）是一种罕见的先天性膈疝，通常主要发生在右侧，女性患病率较高。通常是偶然诊断的，MH可能与先天性心脏缺陷共存，胸壁异常和某些遗传综合征，如唐氏综合征。一名患有唐氏综合症的4岁男孩同时接受了MH修复和室间隔缺损（VSD）闭合。进行了垂直中线胸骨切开术，室间隔缺损采用右心房入路修复。随后，进行了MH修复。手术三周后,这个病人出现了完全的心脏传导阻滞,这导致了VVI起搏器的植入。