关键词: Behçet’s disease epididymitis hemoptysis orchitis pulmonary artery aneurysm vasculitis

来  源:   DOI:10.1177/2050313X241257441   PDF(Pubmed)

Abstract:
Behçet\'s disease is a chronic systemic inflammatory vasculitis of unknown etiology. It is characterized by recurrent episodes of oral aphthous ulcers, genital ulcers, skin lesions, ocular lesions, and other manifestations. This disease affects many organs and systems, showing a wide range of clinical features. Although pulmonary artery involvement is not common in Behçet\'s disease, its presence carries a substantial risk of mortality. This report provides a detailed history of a 25-year-old male who was admitted with productive cough, hemoptysis, dyspnea on minimal exertion, fever, and chest pain. He had recurrent orchitis and epididymitis for 7 years, as well as oral and genital ulcers and severe headache. Clinical examination revealed decreased breath sounds at the right middle lung. Thoracic computed tomography angiography confirmed multiple pulmonary artery aneurysms bilaterally. The patient was diagnosed with Behçet\'s disease, and immunosuppression therapy was initiated. During follow-up, the patient did not report any complications. This case report underscores the significance for clinicians to consider Behçet\'s disease as a differential diagnosis in patients presenting with hemoptysis and a history of orchitis and epididymitis, given that Behçet\'s disease rarely causes pulmonary artery aneurysms.
摘要:
Behçet病是一种病因不明的慢性全身性炎症性血管炎。它的特点是口腔口疮溃疡反复发作,生殖器溃疡,皮肤损伤,眼部病变,和其他表现。这种疾病影响许多器官和系统,表现出广泛的临床特征。尽管肺动脉受累在Behçet病中并不常见,它的存在带来了巨大的死亡风险。本报告提供了一名25岁男性因生咳入院的详细病史,咯血,轻微劳累时呼吸困难,发烧,和胸痛。他有复发性睾丸炎和附睾炎7年,以及口腔和生殖器溃疡和严重头痛。临床检查显示右中肺呼吸音减少。胸部CT血管造影证实双侧多发肺动脉动脉瘤。病人被诊断出患有Behçet病,并开始免疫抑制治疗。随访期间,患者未报告任何并发症.该病例报告强调了临床医生将Behçet病作为出现咯血并有睾丸炎和附睾炎病史的患者的鉴别诊断的重要性。鉴于Behçet病很少引起肺动脉动脉瘤。
公众号