关键词: Erdheim-Chester disease aortitis cardiorenal syndrome dabrafenib heart failure with reduced ejection fraction

来  源:   DOI:10.1016/j.jaccas.2024.102374   PDF(Pubmed)

Abstract:
A 54-year-old woman with a diagnosis of Erdheim-Chester disease under therapy with dabrafenib presents with clinical signs of heart failure. After discontinuing the offending medication and initiating guideline-directed medical therapy for heart failure with reduced ejection fraction, the clinical picture improved.
摘要:
一名54岁的女性在接受dabrafenib治疗时被诊断为Erdheim-Chester病,表现出心力衰竭的临床症状。在停止使用有问题的药物并开始指导指南的药物治疗射血分数降低的心力衰竭后,临床表现有所改善。
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