PDF(Pubmed)
Abstract：
Fibrolamellar carcinoma is a rare liver tumor, with most cases arising in people younger than 40 years of age. We present a case series of five patients with histological confirmation of fibrolamellar carcinoma who had liver resection as the primary treatment. The median age of diagnosis was 24 years with nonspecific clinical manifestations in otherwise healthy patients. Alpha-fetoprotein levels were widely variable. Patients had classical imaging, macroscopic, and microscopic findings. Most of our patients underwent a hemihepatectomy and 60% recurred after the first year.
摘要：
纤维层癌是一种罕见的肝脏肿瘤，大多数病例出现在40岁以下的人群中。我们介绍了一系列病例，包括5例组织学证实为纤维板层癌的患者，这些患者以肝脏切除术为主要治疗方法。在其他健康患者中，诊断的中位年龄为24岁，临床表现无特异性。甲胎蛋白水平变化很大。患者有经典影像学检查，宏观，和微观发现。我们的大多数患者接受了半肝切除术，第一年后有60％复发。
