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Abstract：
Scurvy is an infrequent pathological condition resulting from a sustained dietary vitamin C deficiency. Radiology becomes pivotal because the diagnostic process for scurvy can be intricate, given its resemblance to bone neoplasms. A 6-year-old boy, reported persistent pain and swelling in the right thigh for 2 months prior to hospitalization. Clinical examination revealed a mass localized in the right thigh and anemia. A radiograph of the right femur demonstrated extensive osteopenic changes, \"Trümmerfeld zone\", \"Frankel line\", \"Pelkin fracture\", \"Wimberger ring sign\", and para-epiphyseal subperiosteal hematoma. The absence of any such cases in our institution over the preceding decade emphasizes the uniqueness of this presentation. Histopathological evaluation yielded atypical results, prompting further radiographic assessment of the left femur and thorax. The subsequent findings corroborated the classic \"scorbutic rosary\" presentation, indicative of scurvy. The patient\'s symptoms gradually resolved with high-dose supplementation of vitamin C. Scurvy predominantly presents with musculoskeletal manifestations. Plasma vitamin C level assessment is the gold standard for the diagnosis, but it is currently inaccessible in our nation. Consequently, radiographic evaluation reveals pathognomonic features of the disorder. In thoracic radiographs, the \"scorbutic rosary\" presentation is evident. In contrast, long bones exhibit hallmarks of scurvy: diffuse osteopenia, \"Frankel line\", \"Trümmerfeld zone\", \"Pelkin fracture\", \"Wimberger ring sign\", and para-epiphyseal subperiosteal hematoma. Prompt intervention with vitamin C thwarts the progression to severe complications. Radiology is an indispensable tool in diagnosing pediatric scurvy, especially in developmental countries where the assessment of vitamin C serum levels is inaccessible.
摘要：
镰刀是一种罕见的病理状况，由持续的膳食维生素C缺乏引起。放射学变得很关键，因为对镰刀病的诊断过程很复杂，因为它与骨肿瘤相似。一个六岁的男孩,报告在住院前2个月的右大腿持续疼痛和肿胀。临床检查显示右侧大腿有肿块，贫血。右股骨的X线片显示广泛的骨质疏松改变，\"Trümmerfeld区\",\"弗兰克尔线\",“骨盆骨折”，\"Wimberger戒指标志\",骨phy旁骨膜下血肿。我们机构在过去十年中没有任何此类案例，这突出了这种介绍的独特性。组织病理学评估产生非典型结果，提示对左股骨和胸部进行进一步的影像学评估。随后的发现证实了经典的“蝎子念珠”的陈述，表明了镰刀。高剂量补充维生素C后，患者的症状逐渐缓解。镰刀病主要表现为肌肉骨骼表现。血浆维生素C水平评估是诊断的金标准,但它目前在我们国家是无法进入的。因此,影像学评估揭示了该疾病的病理特征。在胸片上,\\\\\\\\\\\\\\\\\\\\\\\\\\\\\\\\\\\\\\\\\\\\\\\\\\\\\\\\\\\\\\\\\\\\\\\\\\\\\\\\\\\\\\\\\\\\\\\\\\\相比之下,长骨表现出镰刀症的标志：弥漫性骨质减少，\"弗兰克尔线\",\"Trümmerfeld区\",“骨盆骨折”，\"Wimberger戒指标志\",骨phy旁骨膜下血肿。维生素C的及时干预阻碍了严重并发症的进展。放射学是诊断小儿镰刀病不可或缺的工具，尤其是在无法评估维生素C血清水平的发展中国家。
