Abstract:
A paraganglioma is a neuroendocrine tumor that may secrete catecholamines and present with symptoms of sympathetic overload such as hypertension and diaphoresis. It is important that paragangliomas are identified, as they must often be treated by surgical excision. IgG4-related retroperitoneal fibrosis (IgG4-RPF) is a systemic inflammatory disease that results in the infiltration of IgG4-positive plasma cells in the retroperitoneum. Such fibrosis may adversely affect nearby organs and tissues. Here, we describe a case of combined paraganglioma and IgG4-RPF in a 47-year-old female patient. This case demonstrates the deleterious effect of these two conditions when they occur simultaneously.
摘要:
副神经节瘤是一种神经内分泌肿瘤,可分泌儿茶酚胺,并伴有交感神经超负荷的症状,如高血压和出汗。确认副神经节瘤很重要,因为它们通常必须通过手术切除来治疗。IgG4相关腹膜后纤维化(IgG4-RPF)是一种全身性炎症性疾病,导致腹膜后IgG4阳性浆细胞浸润。这种纤维化可能不利地影响附近的器官和组织。这里,我们描述了一例47岁女性患者的副神经节瘤和IgG4-RPF合并病例.这种情况证明了这两种情况同时发生时的有害影响。