关键词: eccrine porocarcinoma metastasis skin adnexal malignancy zosteriform

来  源:   DOI:10.1111/ijd.17259

Abstract:
Eccrine porocarcinoma (EPC) is a rare skin adnexal malignancy with a high potential for metastases. The most common metastatic sites are the lymph nodes and lungs. CCutaneous metastasis is extremely rare, particularly the zosteriform variant, with fewer than 5 cases reported in the literature. Here, we report a unique case of EPC in a 71-year-old male, clinically presenting with multiple clusters of ulcerated nodules distributing as a zosteriform pattern throughout his upper left limb, along with draining lymphatic metastases and lymphedema.
摘要:
内分泌癌(EPC)是一种罕见的皮肤附件恶性肿瘤,具有很高的转移潜力。最常见的转移部位是淋巴结和肺。淋巴结转移极为罕见,特别是zosteriform变体,文献报道的病例少于5例。这里,我们报告了一个71岁男性的独特EPC病例,临床上表现为多个聚集的溃疡结节,在他的左上肢呈带状疱疹样分布,伴随着淋巴转移和淋巴水肿。
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