关键词: bronchiectasis chronic sinusitis kartagener syndrome primary ciliary dyskinesia situs inversus

来  源:   DOI:10.7759/cureus.58747   PDF(Pubmed)

Abstract:
Kartagener syndrome (KS), also known as primary ciliary dyskinesia, is a rare genetic disorder commonly diagnosed early in childhood. It is characterized by a triad of findings, namely, situs inversus, chronic sinusitis, and bronchiectasis. Here, we present the case of a 73-year-old female who incidentally presented the KS triad during her imaging tests in the emergency department of our institution for COVID-19 symptoms.
摘要:
Kartagener综合征(KS),也称为原发性纤毛运动障碍,是一种罕见的遗传性疾病,通常在儿童早期被诊断出来。它的特点是三位一体的发现,即,situsinversus,慢性鼻窦炎,还有支气管扩张.这里,我们介绍了一例73岁的女性,她在我院急诊科进行的COVID-19症状影像学检查中偶然出现KS三联征.
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