PDF(Pubmed)
Abstract：
Tricuspid atresia, a critical congenital heart defect (CHD), accounts for approximately 1% of all cases of CHDs. When tricuspid atresia is coupled with numerous other unexpected congenital cardiac anomalies, a patient\'s condition becomes more serious and more complex. We present a case that demonstrates the stepwise approach to the holistic treatment of congenital tricuspid atresia in the presence of normally related great vessels, a large ventricular septal defect (VSD), atrial septal defect (ASD), and trivial patent ductus arteriosus (PDA). While expanding upon the implementation of chest X-ray imaging, serial transthoracic echocardiogram (TTE) imaging, and the balloon atrial septostomy (BAS) procedure, we also provide insight into the multidisciplinary team-based approach utilized for this patient\'s case. This case illustrates a rare critical CHD coupled with other, more common congenital anomalies, and suggests that with multidisciplinary management and treatment, it is possible the mortality rates associated with this diagnosis could decline.
摘要：
三尖瓣闭锁,严重的先天性心脏病(CHD),约占所有CHD病例的1%。当三尖瓣闭锁伴有许多其他意外的先天性心脏异常时，病人的病情变得更加严重和复杂。我们提出了一个案例，证明了在存在正常相关的大血管的情况下，先天性三尖瓣闭锁的整体治疗的逐步方法。大型室间隔缺损(VSD),房间隔缺损(ASD),和微小动脉导管未闭（PDA）。在扩大胸部X射线成像的实施时，连续经胸超声心动图(TTE)成像,和气囊式房间隔造口术(BAS),我们还提供了对该患者病例采用的多学科团队方法的洞察.这个案例说明了一个罕见的关键CHD与其他，更常见的先天性异常，并建议通过多学科管理和治疗，与这种诊断相关的死亡率可能会下降。
