PDF(Pubmed)
Abstract：
Arrhythmogenic right ventricular cardiomyopathy is an important differential diagnosis in young patients presenting with palpitations and/or dyspnea and must be appropriately investigated. A 23-year-old man presented with cardiogenic shock and monomorphic ventricular tachycardia. He reported palpitations and progressive dyspnea for more than two years, but those symptoms were attributed to anxiety without any further investigation by his family physician. Investigations after the catastrophic presentation in our center suggested terminal right-sided heart failure with severe hepatic insufficiency and acute kidney injury. The patient benefited from extracorporeal membrane oxygenation, followed by an urgent heart transplant 16 days later after the exclusion of liver cirrhosis. Histopathologic analysis of the explanted heart confirmed arrhythmogenic cardiomyopathy.
摘要：
致心律失常性右心室心肌病是出现心悸和/或呼吸困难的年轻患者的重要鉴别诊断，必须进行适当的检查。一名23岁男子出现心源性休克和单形性室性心动过速。他报告心悸和进行性呼吸困难超过两年，但这些症状是由于焦虑引起的,没有他的家庭医生进行进一步的调查.在我们中心的灾难性表现后的调查显示，晚期右侧心力衰竭伴有严重的肝功能不全和急性肾损伤。患者受益于体外膜氧合，随后在排除肝硬化16天后进行紧急心脏移植。移植心脏的组织病理学分析证实了致心律失常性心肌病。
