关键词: Rosai-Dorfman disease extranodal histiocytosis histiocytosis oral neoplasm

Mesh : Humans Histiocytosis, Sinus / surgery pathology Female Middle Aged Tomography, X-Ray Computed

来  源:   DOI:10.1016/j.bjoms.2024.04.014

Abstract:
Rosai-Dorfman disease (RDD) is a rare histiocytic disorder with an unclear aetiology, and commonly presents with painless, bilateral cervical lymphadenopathy. Extranodal presentation in the absence of nodal involvement has been reported to have a predilection for the head and neck with less than 20 cases involving the jaw bones and sinuses. We present an interesting case of unifocal RDD of the infratemporal space in the absence of nodal involvement in a 61-year-old female treated with surgical excision and adjuvant radiation therapy.
摘要:
Rosai-Dorfman病(RDD)是一种罕见的组织细胞疾病,病因不明,通常表现为无痛,双侧颈淋巴结肿大。据报道,在没有淋巴结受累的情况下,结外表现倾向于头颈部,涉及颌骨和鼻窦的病例少于20例。我们介绍了一个有趣的案例,即在没有接受手术切除和辅助放射治疗的61岁女性淋巴结受累的情况下,颞下空间的单焦点RDD。
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