Abstract：
A female patient, known to have hypermobile Ehlers-Danlos syndrome (hEDS), underwent several elective gastroscopies under sedation in different hospitals. Except for a single incident of mild laryngospasm during emergence, all procedures were uneventful. On that occasion, following the procedure in the postanesthesia care unit, the patient suffered severe airway obstruction, and standard airway rescue techniques exacerbated adequate ventilation. After the removal of all stimuli and maintaining only an indirect oxygen supply via a mask in front of her face, her airway improved, and the patient fully recovered after 17 minutes. After the gastroscopy, physical examination revealed that the patient had an extremely flexible trachea that could be completely moved outside the midline to the extreme right and left. For the subsequent procedures, an airway plan was developed in conjunction with the patient and resulted in uncomplicated perianesthetic care. This case report serves to alert readers to the risk of adverse airway events in patients with EDS and suggests an alternative approach to avoid such complications. When patients receive care in different hospitals, adequate documentation is essential and adequate preoperative assessment is crucial. This case study demonstrates the value of patient-coproduction care plans.
摘要：
一位女性患者,已知患有超机动Ehlers-Danlos综合征（hEDS），在不同医院的镇静下接受了几次选择性胃镜检查。除了在出现时发生了一次轻度喉痉挛，所有程序都很顺利。在那个场合,按照麻醉后监护室的程序，患者出现严重的气道阻塞,标准的气道救援技术加剧了充分的通气。在消除所有刺激并仅通过面罩在她面前保持间接氧气供应之后，她的气道改善了,17分钟后患者完全康复。胃镜检查后,体格检查显示，病人有一个非常灵活的气管，可以完全移动到中线之外，向右和向左。对于后续程序，与患者一起制定了气道计划，并导致了简单的麻醉护理。此病例报告旨在提醒读者EDS患者发生不良气道事件的风险，并提出了避免此类并发症的替代方法。当病人在不同的医院接受治疗时，充分的文献记录是必要的,充分的术前评估是至关重要的.此案例研究证明了患者共同生产护理计划的价值。
