PDF(Pubmed)
Abstract：
This case report presents a rare complication of hepatic cystic echinococcosis in a 12-year-old Latino male, residing in a nonendemic region, who developed long-term sequelae of portal vein thrombosis accompanied by the emergence of a hyper-vascular sigmoid colon mass. Portal vein involvement in hepatic cystic echinococcosis is exceedingly uncommon, with limited documented cases. The presentation of the patient included intermittent hematochezia, abdominal pain, and fatigue. Imaging revealed liver cysts and chronic portal vein thrombosis with cavernous transformation, resulting in portal hypertension. Notably, the patient also exhibited mesenteric venous thrombosis, further complicating the clinical picture. The diagnosis was confirmed through echinococcus serology testing. Treatment involved a six month course of Albendazole, puncture-aspiration-injection-reaspiration procedure, splenectomy, and splenorenal shunt to alleviate portal hypertension. This case underscores the significance of considering portal hypertension secondary to hepatic cystic echinococcosis, even in nonendemic regions, particularly in pediatric patients with unique clinical presentations.
摘要：
该病例报告显示了一名12岁拉丁裔男性的罕见肝囊性包虫病并发症，居住在非流行地区，长期发展为门静脉血栓形成的后遗症，并伴有血管过多的乙状结肠肿块的出现。肝囊性包虫病的门静脉受累非常罕见，有限的记录在案的案件。患者的表现包括间歇性便血，腹痛,和疲劳。影像学显示肝囊肿和慢性门静脉血栓形成伴海绵样变，导致门静脉高压.值得注意的是,患者还表现出肠系膜静脉血栓形成，进一步复杂化的临床表现。通过棘球球菌血清学检测证实了诊断。治疗包括阿苯达唑六个月的疗程，穿刺-抽吸-注射-再呼吸程序，脾切除术,和脾肾分流术缓解门静脉高压。该病例强调了考虑肝囊型包虫病继发门静脉高压的重要性，即使在非流行地区，特别是在具有独特临床表现的儿科患者中。
